Neuroblastoma and Life-Threatening Tracheal Obstruction: A case report and literature review

Neuroblastoma and Life-Threatening Tracheal Obstruction: A case report and literature review

Abstracts / International Journal of Pediatric Otorhinolaryngology 75 (2011) 725–729 Aggressive psammomatoid ossifying fibroma in a 3-month-old boy—A...

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Abstracts / International Journal of Pediatric Otorhinolaryngology 75 (2011) 725–729

Aggressive psammomatoid ossifying fibroma in a 3-month-old boy—A case report Lidia Zawadzka-Glos a,*, Eliza Brozek-Madry a, Mieczyslaw Chmielik a, Michał Brzewski a, Agnieszka Biejat a, Jadwiga Maldyk b a Department of Pediatric Otolaryngology, Warsaw Medical University, Poland b Department of Pathology, Warsaw Medical University, Poland Aggressive psammomatoid ossifying fibroma (APOFs) is a benign mesenchymal tumor of the bone with a large growth potential, occurring usually in young adolescents and children. In this case report we are presenting a 3-month-old boy who was diagnosed with an aggressive psammomatoid ossifying fibroma of the nose and paranasal sinuses. In this age early diagnosis is difficult and may results in misdiagnosis such as chronic rhinitis. Endoscopic approach was chosen to remove the tumor. This case report demonstrates that complete endoscopic removal of large tumor involving nasal cavity and paranasal sinuses is effective, though technically challenging. doi:10.1016/j.ijporl.2010.05.044

Neuroblastoma and life-threatening tracheal obstruction: A case report and literature review Claire Kinsella a,*, John Russell b, Dave Mannion c, Michael Capra a a Department of Haematology/Oncology, Our Lady’s Children’s Hospital, Crumlin, Dublin 12, Ireland b Department of Otorhinolaryngology, Our Lady’s Children’s Hospital, Crumlin, Dublin 12, Ireland c Department of Anaesthesiology, Our Lady’s Children’s Hospital, Crumlin, Dublin 12, Ireland Thoracic neuroblastoma is a rare cause of life-threatening tracheal compression in paediatric oncology. We describe the case of a 5-month old boy with a 2-week history of progressive stridor, a right supraclavicular mass, a paravertebral/mediastinal mass on imaging and elevated urinary catecholamines. In view of the patient’s threatened airway, a multidisciplinary management plan was agreed upon prior to obtaining a biopsy to confirm the diagnosis of neuroblastoma. Preoperative microlaryngobronchoscopy (MLB) demonstrated critical tracheal compression necessitating intubation. Neuroblastoma was confirmed on histology. Urgent cytoreductive treatment was initiated with excellent response allowing extubation 14 days later. doi:10.1016/j.ijporl.2010.06.016

Combined sphenoid and frontal sinus aplasia accompanied by bilateral maxillary sinus hypoplasia in a child with sinusitis Arzu Tatlıpınar a,*, Onur Dede a, Erkan Esen a, Tanju Go¨kc¸eer a, Tayfun Akog˘lu b a Haydarpas¸a Numune Research and Training Hospital, 1st ENT Clinic, U¨sku¨dar, I˙stanbul, Turkey b Haydarpas¸a Numune Research and Training Hospital, Radiology Clinic, U¨sku¨dar, I˙stanbul, Turkey Paranasal sinus agenesis is unusual clinical condition. The frontal sinus agenesis is more frequently seen, whereas agenesis of

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sphenoid sinus is extremely rare. Agenesis of both frontal and sphenoid sinus is very unique. This case presents a 13-year-old child with combined sphenoid and frontal sinus agenesis accompanied by bilateral maxillary sinus hypoplasia with scoliosis and coccyx abnormality.

doi:10.1016/j.ijporl.2010.06.017

Primary paranasal sinus meningioma of a 1.7-year-old boy Mu Xian, Bing Zhou * Beijing Tong Ren Hospital, Capital Medical University, Key Laboratory of Otolaryngology Head and Neck Surgery (Capital Medical University), Ministry of Education, China

A 1.7-year-old boy was admitted to our hospital with the first impression of ossified fibroma in the right ethmoid sinus. However, histopathological examination of the surgical specimen turned out to be meningioma. The mass was completely removed endoscopically assisted by image-guided navigation system. This is the youngest ectopic meningioma case reported. The clinic figure and treatment of primary paranasal sinus meningioma is briefly discussed. Considering the young age and small blood volume of this patient, careful preoperative preparation and the cooperation of multi disciplines were of vital importance. doi:10.1016/j.ijporl.2010.06.018

Pharyngeal tonsil manifestation of Langerhans cells sarcoma: A case report and review of the literature Ba Luo a,b, Bian Pian b, Zhou Peng a, Du Jintao a, Liu Shixi a,* a Department of Otorhinolaryngology-Head and Neck Surgery of West China Hospital of Sichuan University, 37# Guoxuexiang, Chengdou, Sichuan, China b Department of Otorhinolaryngology of People’s Hospital of The Tibet Autonomous Region, 18# Linkor Northern Road, Lhasa, China Langerhans cell sarcoma (LCS) is an extremely rare malignant disease with multi-organ involvement and a poor prognosis. LCS involvement of tonsil has not been previously reported. However, we present herein a 10-year-old Tibetan boy distressed by LCS arising on the pharyngeal tonsil. Owing to local traditions and customs, he endured a long period of treatment with traditional Tibetan medicine which provided only slight relief at best that delayed an accurate diagnosis and scientific medical treatment. Subsequently, based on CT and MRI scans, combined with pathology features positive immunophenotype for the CD1a and S-100 proteins confirmed the diagnosed of LCS. We performed a surgical resection along with a regimen of E-CHOP chemotherapy was prescribed as new protocols. As a result the patient complete remission symptoms and without relapse has been 20 months. doi:10.1016/j.ijporl.2010.06.019