International Journal of Pediatric Otorhinolaryngology (2007) 71, 1325—1330
IJPORL Extra Abstracts IJPORL Extra is the online companion publication to the International Journal of Pediatric Otorhinolaryngology. IJPORL Extra publishes case reports which have an important educational value but cannot be published in the printed journal due to lack of space. Case reports published in the Extra will be peer reviewed in the usual way and can be cited through digital object identifiers (DOI), as can articles published in the printed edition of the regular Journal. These DOIs are published at the foot of each article. Some abstracting and indexing services, such as Medline, do not currently include such publications in their database. For this reason we have decided to include the abstracts of articles published in Extra in the printed edition of the journal. IJPORL Extra is available at http://www. sciencedirect.com/science/journal/18714048 on a complementary basis for entitled institutions subscribing electronically to the regular journal, and on an article pay-per-view basis for others.
We describe a case report of a three and a half year old child who was referred to the otolaryngology clinic with two papillomatous projections in her left nostril. The girl was diagnosed as having Hyper IgE syndrome which is a rare immunodeficiency disorder characterized by elevated levels of IgE in blood serum and multiple skeletal, pulmonary and cutaneous manifestations. The tumors in her nose were excised and the final diagnosis was Peripheral T-cell Lymphoma. To our knowledge this is the first report of a toddler with Hyper IgE syndrome and this type of Lymphoma. DOI: 10.1016/j.ijporl.2007.02.031
Solitary plexiform neurofibroma of the nasal tip: Case report and review of the literature
Charbel Rameh, Sami Husseini, Ayman Tawil, Nabil Fuleihan, Usamah Hadi * American University of Beirut Medical Center, Bliss Street, Beirut, Lebanon
Peripheral T-cell lymphoma presenting as nasal papilloma in a child with hyper IgE syndrome Nili Segal a,*, Moshe Puterman a, Albert Gatot a, Joseph Kapelushnik c, Daniel Benharroch b a Department of Otolaryngology, Head and Neck Surgery, Soroka University Medical Center, BenGurion University of the Negev, Beer-Sheva, Israel b Department of Pathology, Soroka University Medical Center, Ben-Gurion University of the Negev, Beer-Sheva, Israel c Pediatric Oncology—Hematology Unit, Soroka University Medical Center, Ben-Gurion University of the Negev, Beer-Sheva, Israel 0165-5876/$ — see front matter
Peripheral nerve sheath tumors of the nose are a rarity. In this article, we report the first case of a plexiform neurofibroma arising from the nasal tip. A literature review highlights the clinical and histological characteristics of this lesion, its differential diagnosis and its management. DOI: 10.1016/j.ijporl.2007.03.022