Abstracts inal) affecting primarily the V1 and V2 branches, in other characteristics that they can present we have the glaucoma, intracranial calcifications and seizure. Its pathogenesis is not yet clarified, is attributed to a genetic component. Case report: A 46 years old female patient who went to the service of the oral maxillofacial surgery, for evaluation and clinical examination showing purplish macular in the right side of the face, coinciding with the path of V1 and V2 branches of the cranial nerve V without crossing the facial midline, presenting mild paresis, increased volume of the affected area as well as glaucoma previously diagnosed. Intraoral we observed violet maculas stain in the right maxilla, we indicated imaging studies. Management of patients with Sturge–Weber syndrome is focused on treating associated neurologic and ocular abnormalities, hypertrophy of vascular tissue in the affected area. Conclusion: The clinical management of all diseases including the syndrome is of vital importance to avoid severe complications, which is why we must expand the knowledge of this disease and currently there is insufficient documentation due to the rarity that is presented. Conflict of interest: None declared. doi:10.1016/j.ijom.2011.07.530
268 Odontogenic central fibroma case report M.I.J. Betancourt Carpio ∗ , J.R. Dopazo, H. Velez Gimon, M. Cachazo, O. Reyes, E.L. De Armas, A.M. Flete Buco Maxilofacial Surgery, Hospital Domingo Luciani, Caracas, Venezuela
Odontogenic central fibroma is a benign odontogenic tumor characterized by strands of epithelium in a fibrous stroma. It is reported in ages between 4 and 80 with an average of 40 years. It has female predilection 2.2. This tumor is characterized by local cortical expansion, swelling inducing dental movement, asymptomatic in most cases. The objective of this paper is to report a case of this unfrequent pathology, as well as the treatment protocol used for the surgical resection. It is described a patient with odontogenic central fibroma, who was referred to the Buco Maxilofacial service of the Domingo Luciani Hospital. Case report: 28-Year-old male patient from La Guaira, Edo Vargas, referred for symptoms associated to the tumor.
In the clinical exam it is observed a swelling in right midface, fast evolution with disappearance of mandibular angle and expansion of bone corticals. It is determined to perform under general anesthesia surgical excision of the injury to afterwards confirm the initial diagnostic by histopathological study. The procedure is finished without complications. To this moment the patient is under observation by a multidisciplinary team with a satisfactory evolution. Conclusion: Odontogenic central fibroma is an extremely rare tumor, which accounts only 0.1% of all odontogenic tumors, the pathogenesis remains unknown. This report underlines the clinical, radiographic and histopathological characteristics to perform an early diagnostic and therefore offer better prognostic to the patient. Conflict of interest: None declared. doi:10.1016/j.ijom.2011.07.531
269 Calcifying epithelial odontogenic tumor: case report M.F. Hernandez ∗ , H. Vélez, M. Cachazo, J. Dopazo, O. Reyes, E. De Armas, A. Flete Hospital General del Este Dr. Domingo Luciani, Caracas, Venezuela
Summary: The calcifying epithelial odontogenic tumor (CEOT), also known as Pindborg tumor, is a rare lesion that represents 1% of odontogenic tumors, although their histogenesis is unknown, the cells that constitute it are derivative of the intermediate layer body enamel. This type of tumor has been found in patients ranging in age from 30 to 50 years of age without gender predilection, and usually located in posterior mandible, sometimes associated with impacted third molars. Among its most common features present slow, progressive and asymptomatic growth, these lesions usually are discovered by the mandibular asymmetry that can potentially cause. Radiographically the tumor appears as a radiolucency with scalloped margins unilocular or multilocular nature, which may contain defects calcified structures with variable size and density, and sometimes containing radiopaque focus, where the treatment of choice is local resection, which results with good prognosis. While CEOT is an uncommon condition, the objective of this study was to determine the typical characteristics such as age, location and radiographic appearance of this various odontogenic tumors,
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since it is extremely valuable to establish differential diagnoses and thereby achieve a plan of successful treatment, and improve the quality of life of patients. Case summary: Male patient aged 45, who presented increased volume in right side of the face, five years of evolution, asymptomatic, slow-growing and progressive as he consults where Incisional biopsy was performed in March 2010, being operated under general anesthesia performing tumor resection and immediate reconstruction with osteosynthesis 2.7 system. Conflict of interest: None declared. doi:10.1016/j.ijom.2011.07.532
270 Midface degloving approach for tumors removal E. Mujica 1,∗ , H. Rivera 2 , R. Rodriguez 2 , M.J. Fernandez 2 , C. Guerrero 2,3 1 OMS Program, Central University of Venezuela, Venezuela 2 Santa Rosa Maxillofacial Surgery Center, Venezuela 3 Orthodontics and OMS Postdoctoral Programs, Central University of Venezuela, Caracas, Venezuela
Statement of the problem: Access to maxillary and adjacent structures has been difficult and limited in terms of direct vision and reaching deeper anatomical structures. Traditional open approaches usually result in facial scars and asymmetric muscles unbalance. The converse midface degloving technique and newer instrumentation allows proper visualization and surgical removal of deeply seeded pathologies in the maxilla and peripheral tissues. Material and method: 4 patients (females) ages 14–36 years old (average 22.5) were treated for tumor removal and immediate reconstruction via midface degloving, two required a Le Fort I Osteotomy with down-fracture and repositioning with plates and screws. All lesions were benign: odontogenic myxoma (2), non-odontogenic myxoma and central giant cell tumor. C-T scans, photographs and standard radiographs were obtained before surgery and every year after surgery. The patients were followed for a minimum of 18 months (18 months to 22 years). Results: All patients showed no recurrence at the latest follow-up, there were no facial scars and the dentition did not suffered secondary to the surgical procedures. Conclusions: The mid-face degloving approach allows adequate visualization for surgical removal of tumors in the maxilla