A case report Infantile fibromatosis of the mandible

A case report Infantile fibromatosis of the mandible

A case of ameloblastic fibroma of the maxilla in a 7-year-old patient is presented. The patient was brought to our hospital complaining of a painless ...

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A case of ameloblastic fibroma of the maxilla in a 7-year-old patient is presented. The patient was brought to our hospital complaining of a painless enlargement of his left cheek for 1 month. The medical history was unremarkable. Radiographic evaluation revealed a radio-opaque area in the left maxillary sinus, and the germ of the second molar was observed at the orbital floor which was expansively elevated by the maxillary sinus tumor. Computed tomography of the paranasal sinus revealed destruction of the posterior wall of the maxillary sinus. The tumor was diagnosed an ameloblastic fibroma by excisional biopsy under general anaesthesia. Through sublabial incision, the tumor was extirpated under general anaesthesia. Intraoperative findings showed the tumor was well capsulized by fibrous tissue and the posterior wall of the maxillary sinus showed defects. Five tooth germs were extirpated with the tumor. Six months after surgery, there was no evidence of tumor recurrence, and there was no facial deformity.

A case report Infantile fibromatosis of the mandible Yu Sate’, Seizi Kishimoto’, Haruo Saito’. Toshiaki Moriki’ ‘Department of Otolaryngology, Kochi Medical School, Kochi ‘Clinical Laboratory, Kochi Medical School, Kochi Infantile fibromatosis is a rare benign tumor and an infancy- and childhood-counterpart of musculoaponeurotic fibromatosis. The tumor does not metastasize, however, it can easily recur locally. We present a case of a 2-year-old boy who came to our attention because he complained of difficulty in opening his mouth. Plain X-ray showed a radiolucent lesion at the body of the left mandible and CT and MRI showed that mandible replaced with homogeneous mass and expanded to the oropharynx cavity. Laboratory examination showed no abnormalities. The pre-operative biopsy was unsuccessful because sufficient amount of tissue for diagnosis could not be obtained. As X-ray findings indicated an odontogenic tumor and the size of the mass gradually increased, an operation was performed. We removed one third of the mandible and reconstructed by means of an iliac bone graft. The extirpated tumor was a solid, ill-defined, scar-like mass that measured about 3.5 cm in diameter. The resulting histological examination gave a diagnosis of infantile fibromatosis. It has been 3 years since the operation, and there has been no recurrence.

Three cases with malignant neoplasms manifesting with sinonasal tract symptoms Hiroshi Kumanomidou, Nobuko Kawashiro, Nobuaki Tsuchihashi, Fumiko Shishiyama Department of Otorhinolarlingology, National Children’s Hospital Yukiko Tsunematsu, Masaaki Kumagai Department of Hematology und Oncology, National Children k Hospital We report three malignant neoplasm cases with nasal and paranasal lesions. Two patients had rhabdomyosarcoma and one metastasis of a pararenal neuroblastoma. These malignant neoplasms manifested with symptoms of cheek swelling, intranasal mass and neurological disorder.