- Email: [email protected]
Congenital rhabdomyoma of the heart
ABSTRACTS
136
obstruction
and
chylothorax.~Thomas
M.
Holder Calcified Postoperative Epicardial Granuloma. 8. 6. Roe. Ann Thorac
Surg
19:472-473
(April),
1975. A case is reported of an 8-yr-old boy who had a calcific granuloma on the external surface of the right ventricle 4 yr following the repair of a ventricular septal defect. The lesion was removed, and a systolic ejection murmur present prior to its removal disappeared. The granuloma is postulated as a response to surgical silk. The murmur is suspected to be based on pressure on the right ventricular outflow tract by this I&cm-diameter mass.--Keith W. Ashcraf Congenital Rhabdomyoma of the Heart. K. D. Bhoolo. S Afr Med J 49:936-938
(May), 1975.
More than 100 cases of cardiac rhabdomyomata have been reported in the English literature. In most cases the tumor is found during postmortem examination of stillborn, newborn, or neonatal patients. This is a single case report of a female infant delivered by cesarean section, the product of a pregnancy complicated by preeclamptic toxemia and maternal diabetes mellitus. The baby developed severe cardiac failure within hours after delivery, culminating in cardiopulmonary death on the seventh day of life. On postmortem examination the heart was markedly increased in size and weight and contained a nonencapsulated tumor 4.3 cm in diameter situated in the interventricular septum. I%stology confirmed the presence of a tumor containing “spider cells,” a characteristic of cardiac rhabdomyomata.M.R.Q. Davies
ALIMENTARY
Volsred Pedersen Congenital
Oesophageal
Stenosis
Tracheobronchial Remnants. A. K.
Thorax 29:720-725
due
to
Deeraniyo.
(November), 1974.
Two patients are reported with a later complication of distal esophageal obstruction apparent following operative treatment for esophageal atresia and tracheoesophageal fistula. One child who died also had rectal atresia and a sigmoid colostomy. In this child there was a crescent of cartilage and tracheobronchial seromucinous glands present at the site of the esophageal stenosis. Dilatation of the stenosis proved difficult and excision is advocated. No similar cases appear to have been reported.J. F. R. Benlley Simultaneous Occurrence of a Congenital Pyloric
TRACT
Web and Hiatal Insufficiency in an Infant. M.
Congenital Atresia of the Oesophagus. Sigmund
Vooge, Kje/f Levorstad, and Leif Efskind. Thorac Cordiovosc Surg 9:68-74, 1975.
X-ray examination and cinefluorography revealed a severe stenosis at the anastomotic site (diameter of the anastomosis less than one-half the diameter of the esophagus below the anastomosis) in 5 patients. a moderate stenosis in I I patients, and no stenosis at all in 17 patients. Some correlation between the ability to swallow and the degree of stenosis is claimed, whereas no correlation was found between swallowing and esophageal motility as seen by intraluminal pressure recordings and cinefluorography. These investigations revealed a normal motor function in the upper segment, absent peristalsis in the intermediate portion just below the anastomosis, and secondary peristaltic waves in the lower segment. One patient with a 6-cm gap between the upper and lower ends who was treated by intrathoracic esophagogastrostomy when 3 days old and 15 mo later by pyloroplasty was doing well and eating normally at 12 yr of age.--Peter
Stand
J
A study was conducted of 33 patients with esophageal atresia (2 without tracheoesophageal fistula) and 3 patients with tracheoesophageal fistula examined I IL24 yr postoperatively. Most of the patients suffered from repeated respiratory infections throughout early childhood. This tendency decreased at 5-10 yr of age. Six patients had a severe dysphagia, 7 a moderate dysphagia, especially when eating more rapidly than normally, and 23 patients were asymptomatic.
K&m&i 595-598
and P. Kuitunen.
Helv Poediotr
Aeta 29:
(December), 1974.
The authors report the case history of an infant who was under observation for many months before the etiology of his intractable vomiting was diagnosed. The first contrast examination of the stomach at the age of Id mo showed hiatal insufficiency but emptying of the stomach was found to be normal. Nevertheless, conservative therapy with positioning of the infant and feeding of solid food did not normalize the situation. Malabsorption tests proved negative. Pneumoencephalography excluded a cerebral cause of the vomiting and splenoportog-
136
obstruction
and
chylothorax.~Thomas
M.
Holder Calcified Postoperative Epicardial Granuloma. 8. 6. Roe. Ann Thorac
Surg
19:472-473
(April),
1975. A case is reported of an 8-yr-old boy who had a calcific granuloma on the external surface of the right ventricle 4 yr following the repair of a ventricular septal defect. The lesion was removed, and a systolic ejection murmur present prior to its removal disappeared. The granuloma is postulated as a response to surgical silk. The murmur is suspected to be based on pressure on the right ventricular outflow tract by this I&cm-diameter mass.--Keith W. Ashcraf Congenital Rhabdomyoma of the Heart. K. D. Bhoolo. S Afr Med J 49:936-938
(May), 1975.
More than 100 cases of cardiac rhabdomyomata have been reported in the English literature. In most cases the tumor is found during postmortem examination of stillborn, newborn, or neonatal patients. This is a single case report of a female infant delivered by cesarean section, the product of a pregnancy complicated by preeclamptic toxemia and maternal diabetes mellitus. The baby developed severe cardiac failure within hours after delivery, culminating in cardiopulmonary death on the seventh day of life. On postmortem examination the heart was markedly increased in size and weight and contained a nonencapsulated tumor 4.3 cm in diameter situated in the interventricular septum. I%stology confirmed the presence of a tumor containing “spider cells,” a characteristic of cardiac rhabdomyomata.M.R.Q. Davies
ALIMENTARY
Volsred Pedersen Congenital
Oesophageal
Stenosis
Tracheobronchial Remnants. A. K.
Thorax 29:720-725
due
to
Deeraniyo.
(November), 1974.
Two patients are reported with a later complication of distal esophageal obstruction apparent following operative treatment for esophageal atresia and tracheoesophageal fistula. One child who died also had rectal atresia and a sigmoid colostomy. In this child there was a crescent of cartilage and tracheobronchial seromucinous glands present at the site of the esophageal stenosis. Dilatation of the stenosis proved difficult and excision is advocated. No similar cases appear to have been reported.J. F. R. Benlley Simultaneous Occurrence of a Congenital Pyloric
TRACT
Web and Hiatal Insufficiency in an Infant. M.
Congenital Atresia of the Oesophagus. Sigmund
Vooge, Kje/f Levorstad, and Leif Efskind. Thorac Cordiovosc Surg 9:68-74, 1975.
X-ray examination and cinefluorography revealed a severe stenosis at the anastomotic site (diameter of the anastomosis less than one-half the diameter of the esophagus below the anastomosis) in 5 patients. a moderate stenosis in I I patients, and no stenosis at all in 17 patients. Some correlation between the ability to swallow and the degree of stenosis is claimed, whereas no correlation was found between swallowing and esophageal motility as seen by intraluminal pressure recordings and cinefluorography. These investigations revealed a normal motor function in the upper segment, absent peristalsis in the intermediate portion just below the anastomosis, and secondary peristaltic waves in the lower segment. One patient with a 6-cm gap between the upper and lower ends who was treated by intrathoracic esophagogastrostomy when 3 days old and 15 mo later by pyloroplasty was doing well and eating normally at 12 yr of age.--Peter
Stand
J
A study was conducted of 33 patients with esophageal atresia (2 without tracheoesophageal fistula) and 3 patients with tracheoesophageal fistula examined I IL24 yr postoperatively. Most of the patients suffered from repeated respiratory infections throughout early childhood. This tendency decreased at 5-10 yr of age. Six patients had a severe dysphagia, 7 a moderate dysphagia, especially when eating more rapidly than normally, and 23 patients were asymptomatic.
K&m&i 595-598
and P. Kuitunen.
Helv Poediotr
Aeta 29:
(December), 1974.
The authors report the case history of an infant who was under observation for many months before the etiology of his intractable vomiting was diagnosed. The first contrast examination of the stomach at the age of Id mo showed hiatal insufficiency but emptying of the stomach was found to be normal. Nevertheless, conservative therapy with positioning of the infant and feeding of solid food did not normalize the situation. Malabsorption tests proved negative. Pneumoencephalography excluded a cerebral cause of the vomiting and splenoportog-