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Primary macroglossia
IVTERN.%TIONAL
und A.
R.
ABSTRACTS
OF
Arch.
Dis.
Ezjasou.
PEDIATRIC
Child.
43:344
The cnsc of a 7-year-old girl with circulatory changes in fingers and toes is described. The symmetry of the distribution of the ischemia, the failrrrc to demonstrate a precipitating cause, and thr frrnctional nature of the circulatory impairmcnt stated to confirm the diagnosis of Raynaud’s tliscase. After five weeks of increasing circulatory disorder, the child was treated with oral Griseofulvin I25 mgs.b.d; skin discolouration and infcsction around the finger nails disappeared within -7 weeks. but returned after treatment was stopped at the end of 4 weeks. Treatment was therefore started again. It is suggested that Griseofulvin probably exerts its effect by direct action on the pcriphrral arteries.--J. Lister.
HEAD
AND
NECK
I'Iuhi,4HY ~IACROGLOSSIA. A. D. Shafer. (June)
This paper reviews
164 cases of proved agencsis
of the lung from the literature
(June) 1968.
7:357
759
SURGERY
Clin.
Red.
1968.
The author has treated 9 children with primary r~~acroglos:;ia. Five of these children had associated omphalocele and 2 had umbilical hernia. These above cases had macroglossia secondary to idiopathic hypertrophy of the muscle fibers. Three types of primary macroglossia are described: (1) one-sided enlargement in association with localized h!p:~rtrophy of the homolateral mandible or half of fact or body, (2) diffuse enlargement associated with generalized muscular hypertrophy, (3) diffuse enlargement without other muscular hyprrtrophy. An anterior wedge resection of the tongue at about 6 months of age to protect against prognathism and speech defects is the treatment of choice according to the nnthor.:\I. Gilbert. ll~~r~~~~no~D~c~ohlk.~0~3 INFECTED NEWBORX INFAXT. Inf. 9:55-O!?, 1968.
A. Prochiantz.
GOITER IN A Ann.
Chir.
The author reports a case of congenital goiter with stnnnitis and abscess formation. The infant was cruet1 Iry surgery (hemithyroidectomy).-A!.
Bcftcx THORAX .kEXESI!, 0F THE LUNG-PRESENTATION OF EIGHT NEW CASES AND REVIEW OF THE LITEHATUHE. David L. Maltz and Alexander S. Nader. Pediatrics 43:175-188 (July) 1968.
and adds 8 unre-
ported cases seen at the Children’s Hospital of Boston. The anomaly occurs equally in the sexes and involves either side with equal frequency. Diagnosis is suggested firmed by angiography
by chest x-ray and and bronchography.
conA-
though many reports include necropsy findings, the anomaly is not uniformly fatal since 24 of th:l 36 patients reported since 1954 were &v-c at the time of reporting. Cardiac catheterization findings in 3 patients are presented. Pulmonary artery hypertension was present in some patients with associated cardiac anomalies-w. K. Sicber. BILATERAL
COXENITAL
INFANT. hl. Kabelka.
PULMONARY
CYU
Z. K. Chir. 6:15-26,
1s AS 1968.
This paper includes an extensive review of the literature especially commenting on the etiology and treatment. The case of a 4-month-old girt is presented who had bilateral solitary lung cysts and who was operated on successfully. Followup after 3 years showed no abnormality.-S. Hofmanr~ and H. B. Ecksfein.
HEART
AND
GREAT
VESSELS
CO.%RCTATION OF THE LOWER THORACIC Aonra IN A CHILD. T. M. Scheinin and P. Vilki. Z. K. Chir. 6:11-14, 1968. A case of a rare low thoracic aortic coarctation i$ ckscribed. A 7-year-old girl had an 8 cm. long stenosis which was opened longitudinally and widened with a dacron patch. Convalescence and further development have been without further comphcation-S. Hoftnan9a and H. B. E&stein. A RARE TYPE OF ATHIAL SEPTAL DEFECT. R.J. M. AlcCormack, D. Thorax 23:3X%352
Pickering, and I. (July) 1968.
1.
Smith.
In this previously unrecorded cardiac anomaly discovered only at necropsy, the inferior venn caval orifice was straddled by the atrial septum, and the right pulmonary veins emptied into the right atrium. The tape about the inferior vena cava prevented recognition at surgical exploration. -W. K. Sieber. PULMONAHY ARTERY BANDING IN CONGENITAI. HEART DISEASE ASSOCIATED WITH PULMONARY HYPERTENSION. J. M. Reid, R. S. Barclay, E. N. Coleman, 1. G. Stevenson, T. M. Welsh, and h’. n4cSwan. Thorax 23338,s391 (July) 1968.
und A.
R.
ABSTRACTS
OF
Arch.
Dis.
Ezjasou.
PEDIATRIC
Child.
43:344
The cnsc of a 7-year-old girl with circulatory changes in fingers and toes is described. The symmetry of the distribution of the ischemia, the failrrrc to demonstrate a precipitating cause, and thr frrnctional nature of the circulatory impairmcnt stated to confirm the diagnosis of Raynaud’s tliscase. After five weeks of increasing circulatory disorder, the child was treated with oral Griseofulvin I25 mgs.b.d; skin discolouration and infcsction around the finger nails disappeared within -7 weeks. but returned after treatment was stopped at the end of 4 weeks. Treatment was therefore started again. It is suggested that Griseofulvin probably exerts its effect by direct action on the pcriphrral arteries.--J. Lister.
HEAD
AND
NECK
I'Iuhi,4HY ~IACROGLOSSIA. A. D. Shafer. (June)
This paper reviews
164 cases of proved agencsis
of the lung from the literature
(June) 1968.
7:357
759
SURGERY
Clin.
Red.
1968.
The author has treated 9 children with primary r~~acroglos:;ia. Five of these children had associated omphalocele and 2 had umbilical hernia. These above cases had macroglossia secondary to idiopathic hypertrophy of the muscle fibers. Three types of primary macroglossia are described: (1) one-sided enlargement in association with localized h!p:~rtrophy of the homolateral mandible or half of fact or body, (2) diffuse enlargement associated with generalized muscular hypertrophy, (3) diffuse enlargement without other muscular hyprrtrophy. An anterior wedge resection of the tongue at about 6 months of age to protect against prognathism and speech defects is the treatment of choice according to the nnthor.:\I. Gilbert. ll~~r~~~~no~D~c~ohlk.~0~3 INFECTED NEWBORX INFAXT. Inf. 9:55-O!?, 1968.
A. Prochiantz.
GOITER IN A Ann.
Chir.
The author reports a case of congenital goiter with stnnnitis and abscess formation. The infant was cruet1 Iry surgery (hemithyroidectomy).-A!.
Bcftcx THORAX .kEXESI!, 0F THE LUNG-PRESENTATION OF EIGHT NEW CASES AND REVIEW OF THE LITEHATUHE. David L. Maltz and Alexander S. Nader. Pediatrics 43:175-188 (July) 1968.
and adds 8 unre-
ported cases seen at the Children’s Hospital of Boston. The anomaly occurs equally in the sexes and involves either side with equal frequency. Diagnosis is suggested firmed by angiography
by chest x-ray and and bronchography.
conA-
though many reports include necropsy findings, the anomaly is not uniformly fatal since 24 of th:l 36 patients reported since 1954 were &v-c at the time of reporting. Cardiac catheterization findings in 3 patients are presented. Pulmonary artery hypertension was present in some patients with associated cardiac anomalies-w. K. Sicber. BILATERAL
COXENITAL
INFANT. hl. Kabelka.
PULMONARY
CYU
Z. K. Chir. 6:15-26,
1s AS 1968.
This paper includes an extensive review of the literature especially commenting on the etiology and treatment. The case of a 4-month-old girt is presented who had bilateral solitary lung cysts and who was operated on successfully. Followup after 3 years showed no abnormality.-S. Hofmanr~ and H. B. Ecksfein.
HEART
AND
GREAT
VESSELS
CO.%RCTATION OF THE LOWER THORACIC Aonra IN A CHILD. T. M. Scheinin and P. Vilki. Z. K. Chir. 6:11-14, 1968. A case of a rare low thoracic aortic coarctation i$ ckscribed. A 7-year-old girl had an 8 cm. long stenosis which was opened longitudinally and widened with a dacron patch. Convalescence and further development have been without further comphcation-S. Hoftnan9a and H. B. E&stein. A RARE TYPE OF ATHIAL SEPTAL DEFECT. R.J. M. AlcCormack, D. Thorax 23:3X%352
Pickering, and I. (July) 1968.
1.
Smith.
In this previously unrecorded cardiac anomaly discovered only at necropsy, the inferior venn caval orifice was straddled by the atrial septum, and the right pulmonary veins emptied into the right atrium. The tape about the inferior vena cava prevented recognition at surgical exploration. -W. K. Sieber. PULMONAHY ARTERY BANDING IN CONGENITAI. HEART DISEASE ASSOCIATED WITH PULMONARY HYPERTENSION. J. M. Reid, R. S. Barclay, E. N. Coleman, 1. G. Stevenson, T. M. Welsh, and h’. n4cSwan. Thorax 23338,s391 (July) 1968.