Small or hypoplastic dens

GAMUT

Small or Hypoplastic

Dens

BY Scott Schlesinger COMMON

Craniocervical abnormality (including occipitalization of the atlas, anterior atlantoaxial fusion) Down syndrome Klippel-Feil syndrome OS odontoideum, congenital or traumatic Rheumatoid arthritis UNCOMMON

Cartilage-hair syndrome Dyggve-Melchior-Claussen Hurler syndrome Metastasis Morquio disease

syndrome

Dens hypoplasis. This patient has Hurter synFig 2. drome (MPS I-HI. The lateral skufi fdm shows a J-shaped sella. Note the smoothly marginated we&corticeted superior margin of the hypoplastic dens (arrowhead).

Mucolipidosis III (pseudo-Hurler polydystroPW Multiple epiphyseal dysplasia congenita Pseudo-Morquio disease Spondyloepiphyseal dysplasia congenita Spondylometaphyseal dysplasia (including KozFrom the Department Cincinnati.

Fig 1. OS odontoidaum. C-3 and C-4 are partly This midline tomogram demonstrates the separate clearly. The patient presented with neurological attributed to Cl -C2 instability.

Seminers

in Roenfgenology.

Vol XXI,

No 4 (October),

fused. ossick signs

1986:

pp 241-242

of Radiology,

University

Hospital,

Scott Schlesinger: Resident in Radiology, University of Cincinnati Medical Center. Address reprint requests to Scott Schlesinger, MD, Department of Radiology, University Hospital. 234 Goodman St, Cincinnati, OH 45267. Q 1986 by Grune & Stratton, Inc. 0037-I 98X/86/21 04-0004%05.00/0 241

SCOTT

242

lowski type, Kneist syndrome, metatropic plasia) Tuberculosis

dys-

REFERENCES 1. Bailey SA: Disproportionate Short Stature. Philadelphia: Saunders, 1973

SCHLESINGER

2. Epstein BS: The Spine. Philadelphia: Lea & Feiberger, _^-_ 1Y76

3. Melhem R, Dorst JP, Scott CI, Jr, et al: Roentgen findings in mucolipidosis III. Radiology 1973;106:153-160 4. Spranger J, Maroteaux P, Der Kaloustian VM: Dyggve-Melchior-Claussen syndrome. Radiology 1975;114:415-421 5. Wackenheim A: Roentgen Diagnosis of the Craniovertebral Region. New York: Springer-Verlag, 1974; 363-366