Obstruktion der oberen Atemwege bei syndromalen Kraniosynostosen

Obstruktion der oberen Atemwege bei syndromalen Kraniosynostosen

478 British Journal of Oral and Maxillofacial Surgery craniosynostoses. A high rate of relapse of midfacial hypoplasia was found in children and ...

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478

British

Journal

of Oral and Maxillofacial

Surgery

craniosynostoses. A high rate of relapse of midfacial hypoplasia was found in children and adolescents after midface-advancement in the present evaluation. Therefore, the indication for Le Fort IIIosteotomy in the growth period should be limited. Correspondence: Dr. Edeltraud Reinhart, Klinik und Poliklinik fur Mund-, Kiefer- u. Gesichtschirurgie, Pleicherwall 2, D-97070 Wtirzburg.

Ophthalmologische F’robleme und Befunde bei kraniofazialen Synostosen, RD. SchZiifer, S. Bau, H. Collmann. (Dtsch Z Mund Kiefer GesichtsChir 1996; 20: 4). In a retrospective study findings in 114 patients with craniofacial synostosis checked in the eye hospital between 1983 and 1993 were analysed. Four syndromes are concerned: M. Apert (26%), M. Crouzon (28%), M. Pfeiffer (10%) and M. Saethre-Chotzen (36%). The patients average age was 1.26 years, 59% of them female. The investigations took place directly before and 3 to 7 days after the skull surgery. Approximately 50% of our patients were examined after another 6 months. External eye examination did not show any abnormalities in 53% of the patients. Eighteen percent presented a striking exophthalmus and 19% had various alterations of the exterior eye. Strabismus was found in about 50% of the persons tested. The retina was normal in 60%65%. Optic nerve edema decreased from 14% and 17% to 8%. Optic nerve atrophies were found in 19% and 22%. Furthermore, visual acuity and refraction were tested and motility disorders were analysed. Overall the importance of regular eye checking of the patients and an early therapy was emphasized. In cases of amblyopia, occlusion therapy is necessary. Comfortable eye glasses especially made for children are prescribed in cases of ametropia. Eye muscle surgery should be done after the completion of interventions on the skull.

Correspondence: Professor Dr. W. D. Schafer, Univ.-Augenklinik, Josef-Schneider-Str. 11, D-97080 Wiirzburg. Orbitadystopien. J. Miihling, GesichtsChir 1996; 20: ,4).

J.

Zijller. (Dtsch Z Mund Kiefer

Dislocation of the orbita are mainly caused by craniofacial synostoses, facial clefts and meningoceles. Due to the malformation an asymmetrical location of the orbitae, hypo- or hypertelorism will result. Computerized tomography as well as magnetic resonance tomography are considered to be major diagnostic tools. For functional and aesthetic rehabilitation, craniofacial operative techniques are used, corresponding to the basic malformation. Major dislocation of the orbita are treated by osteotomy of the bony orbita and translocation into the right position. Correspondence: Professor Dr. Dr. Joachim Mtihling, Klinik und Poliklinik fur Mund-, Kiefer- und Gesichtschirurgie der Universitat Heidelberg, Im Neuenheimer Feld 400, D-69120 Heidelberg. Obstruktion der oberen Atemwege bei syndromalen Kraniosynostosen. M. Zellner. (Dtsch Z Mund Kiefer GesichtsChir 1996; 20: 4). Obstructive sleep apnoea (OSA) is a frequent finding in craniosynostosis such as Apert syndrome and Crouzon’s disease. Unfortunately, delayed diagnosis may result in potentially serious cardio-pulmonal sequelae. This report reviews the aetiology, diagnosis and therapy with respect to craniosynostosis in OSA. Patient management is best individualized utilizing both surgical and nonsurgical treatment following contributions from affiliated disciplines. Correspondence: Dr. med. Max Zellner, Universitlts-HNO-Klinik, Josef-Schneider-Str. 11, D-97080 Wtirzburg.