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HYDROCEPHALUS ASSOCIATED WITH GOLDENHAR SYNDROME: A CLINICAL CASE REPORT
OOOO Volume 129, Number 1
ABSTRACTS
e119
manifestations and the care needed to perform surgical procedures in the affected areas of the mouth.
RODRIGUES CANUTO, JOYCE HELENA MONTEIRO BARBOSA and, ERICK NELO PEDREIRA
LIPONEUROFIBROMA ON THE HARD PALATE: CASE REPORT OF A RARE MICRO SCOPIC VARIANT. JESSICA HELENA DOTTA, CAMILA DE OLIVEIRA BARBEIRO, HEITOR ALBERGONI DA SILVEIRA, TULIO MORANDIN FERRISSE, JORGE ELAINE SGAVIOLI MASSUCATO and, ESQUICHE LEON, ANDREIA BUFALINO
Hydrocephalus is a pathology characterized by increased head circumference and intracranial pressure with cerebrospinal fluid expansion. Goldenhar syndrome is a congenital anomaly due to errors in morphogenesis, causing variations in the face, ears, and vertebra, constantly associated with other congenital visceral malformations. This article aims to describe the case of a 5-year-old boy diagnosed as having hydrocephalus associated with Goldenhar syndrome. He was referred by a multidisciplinary medical team for the dental evaluation to adapt the oral environment because of the high tooth decay occurrence. This adequacy was achieved through prophylaxis, fluoride application, supervised brushing, restorations, periapical radiographs for exodontia, and educational activities with those who take care of the patient. The team concluded that treatment should be carried out with a multidisciplinary approach, seeking to improve the appearance and functionality of the affected structures and aiming at preventive control to ensure their psychosocial integration.
Neurofibroma is a common cutaneous benign tumor of neural origin, and sporadic cases of fatty variants have been reported. A 56-year-old white woman was referred for evaluation of a nonulcerated submucosal nodule on the hard palate with 2 years of duration without symptoms. Her medical and family history was noncontributory. Intraoral examination revealed a nodular submucosal mass covered by normal-appearing mucosa measuring 2 cm in greatest dimension and resilient in consistency. Radiographic examination did not show alteration. An excisional biopsy was performed, and microscopic analysis showed spindle cell proliferation with regularly scattered adipocytes. By immunohistochemistry, S100 and CD34 were positive and Ki-67 was < 2%. Thus, the diagnosis of liponeurofibroma was established. The lesion healed completely after 4 months of follow-up. This case report shows that fatty change in neurofibroma may occasionally occur, but no impact on its prognosis is observed.
ADENOMATOID ODONTOGENIC TUMOR WITH AREAS OF CALCIFYING EPITHELIAL ODONTOGENIC TUMOR. INGRID DE e FREITAS CAVALHEIRO SAYAO, NATHALIA FIGUEIREDO DE BRITO, JORGE ALEXANDRE MIRANDA, LUIZ FERNANDO DELUIZ, JULIANA DE NORONHA SANTOS NETTO, FABIO RAMOA PIRES and, AGUIDA MARIA MENEZES AGUIAR MIRANDA Odontogenic tumors are a group of neoplasms that eventually can present a combination of histopathologic patterns because of their distinct origins. An 18-year-old woman complaining of unerupted teeth attended the clinic. Medical history was noncontributory. Clinical examination showed absence of teeth 12 and 13 in addition to swelling in the alveolar ridge and palate in the corresponding region. Periapical, occlusal, and panoramic radiographs and cone beam computed tomography showed a well-defined radiolucent area with radiopaque foci, associated to unerupted teeth 12 and 13, causing expansion of both vestibular and palatine cortices. Provisional diagnosis was adenomatoid odontogenic tumor, and an excisional biopsy was performed under local anesthesia. Histopathologic findings showed adenomatoid odontogenic tumor with areas of calcifying epithelial odontogenic tumor. The patient is under follow-up in a multidisciplinary team with no signs of recurrence.
HYDROCEPHALUS ASSOCIATED WITH GOLDENHAR SYNDROME: A CLINICAL CASE REPORT. LUIZA MADALENA MENDES DA VERA CRUZ, CRISLYNE MENDES DA VERA CRUZ, ALEXANDRA GABRIELLY DE SOUSA BENTES, ANTONIA PATRICIA OLIVEIRA BARROS, VANESSA SANTOS
LEIOMYOSARCOMA IN THE LATERAL BORDER OF THE TONGUE: A RARE CASE REPORT. CYNTIA HELENA PEREIRA DE CARVALHO, GEORGE BORJA DE FREITAS, HEVIO FREITAS DE LUCENA, KEILA AMORIM BARROSO, BARBARA VANESSA DE BRITO MONTEIRO, LEORIK e FERREIRA DO PEREIRA DA SILVA and, GEORGE JOAO NASCIMENTO Leiomyosarcoma is a rare mesenchymal malignant neoplasm, of which 3% to 10% of cases occur in the head and neck region. The leiomyosarcoma of the tongue is a very rare tumor with only 10 cases described in the literature. This work reports a case of oral leiomyosarcoma arising in the lateral border of the tongue of a 78-year-old man. Clinical examination showed a well-demarcated, firm and painful nodule measuring about 3 cm in diameter. After incisional biopsy, microscopic analysis showed the spindleshaped tumor cells were arranged in an interlacing fascicular pattern and contained oval to elongated blunt-ended (cigar-shaped) nuclei. More than 10 mitoses per high-power field were counted. Immunohistochemical examination displayed that tumor cells were strongly positive to H-caldesmon, actin, and vimentin and negative to S100, establishing the final diagnosis of leiomyosarcoma. The patient was referred for oncologic treatment.
CHONDROID CHORISTOMA IN THE BORDER OF TONGUE: A RARE CASE REPORT. YURI KALININ, NATALIA LACERDA DE OLIVEIRA, CLAUDIA PEREZ TRINDADE FRAGA, MARINA HELENA CURY GALLOTTINI, ANDERSON DA COSTA LINO COSTA, LETICIA DRUMOND DE ABREU e and, OPHIR RIBEIRO JUNIOR GUIMARAES Choristoma is defined as a histologically normal tissue proliferation, which is not normally found in the anatomic site of proliferation. Chondroid choristoma of the oral soft tissue is a rare lesion, presenting cartilage where it is not expected. The patient was a 31-year-old white man presenting an endophytic firm mass on the right lateral border of the tongue also affecting the ventral surface that had appeared 5 years earlier, which was asymptomatic and measured approximately 3 cm in diameter.
ABSTRACTS
e119
manifestations and the care needed to perform surgical procedures in the affected areas of the mouth.
RODRIGUES CANUTO, JOYCE HELENA MONTEIRO BARBOSA and, ERICK NELO PEDREIRA
LIPONEUROFIBROMA ON THE HARD PALATE: CASE REPORT OF A RARE MICRO SCOPIC VARIANT. JESSICA HELENA DOTTA, CAMILA DE OLIVEIRA BARBEIRO, HEITOR ALBERGONI DA SILVEIRA, TULIO MORANDIN FERRISSE, JORGE ELAINE SGAVIOLI MASSUCATO and, ESQUICHE LEON, ANDREIA BUFALINO
Hydrocephalus is a pathology characterized by increased head circumference and intracranial pressure with cerebrospinal fluid expansion. Goldenhar syndrome is a congenital anomaly due to errors in morphogenesis, causing variations in the face, ears, and vertebra, constantly associated with other congenital visceral malformations. This article aims to describe the case of a 5-year-old boy diagnosed as having hydrocephalus associated with Goldenhar syndrome. He was referred by a multidisciplinary medical team for the dental evaluation to adapt the oral environment because of the high tooth decay occurrence. This adequacy was achieved through prophylaxis, fluoride application, supervised brushing, restorations, periapical radiographs for exodontia, and educational activities with those who take care of the patient. The team concluded that treatment should be carried out with a multidisciplinary approach, seeking to improve the appearance and functionality of the affected structures and aiming at preventive control to ensure their psychosocial integration.
Neurofibroma is a common cutaneous benign tumor of neural origin, and sporadic cases of fatty variants have been reported. A 56-year-old white woman was referred for evaluation of a nonulcerated submucosal nodule on the hard palate with 2 years of duration without symptoms. Her medical and family history was noncontributory. Intraoral examination revealed a nodular submucosal mass covered by normal-appearing mucosa measuring 2 cm in greatest dimension and resilient in consistency. Radiographic examination did not show alteration. An excisional biopsy was performed, and microscopic analysis showed spindle cell proliferation with regularly scattered adipocytes. By immunohistochemistry, S100 and CD34 were positive and Ki-67 was < 2%. Thus, the diagnosis of liponeurofibroma was established. The lesion healed completely after 4 months of follow-up. This case report shows that fatty change in neurofibroma may occasionally occur, but no impact on its prognosis is observed.
ADENOMATOID ODONTOGENIC TUMOR WITH AREAS OF CALCIFYING EPITHELIAL ODONTOGENIC TUMOR. INGRID DE e FREITAS CAVALHEIRO SAYAO, NATHALIA FIGUEIREDO DE BRITO, JORGE ALEXANDRE MIRANDA, LUIZ FERNANDO DELUIZ, JULIANA DE NORONHA SANTOS NETTO, FABIO RAMOA PIRES and, AGUIDA MARIA MENEZES AGUIAR MIRANDA Odontogenic tumors are a group of neoplasms that eventually can present a combination of histopathologic patterns because of their distinct origins. An 18-year-old woman complaining of unerupted teeth attended the clinic. Medical history was noncontributory. Clinical examination showed absence of teeth 12 and 13 in addition to swelling in the alveolar ridge and palate in the corresponding region. Periapical, occlusal, and panoramic radiographs and cone beam computed tomography showed a well-defined radiolucent area with radiopaque foci, associated to unerupted teeth 12 and 13, causing expansion of both vestibular and palatine cortices. Provisional diagnosis was adenomatoid odontogenic tumor, and an excisional biopsy was performed under local anesthesia. Histopathologic findings showed adenomatoid odontogenic tumor with areas of calcifying epithelial odontogenic tumor. The patient is under follow-up in a multidisciplinary team with no signs of recurrence.
HYDROCEPHALUS ASSOCIATED WITH GOLDENHAR SYNDROME: A CLINICAL CASE REPORT. LUIZA MADALENA MENDES DA VERA CRUZ, CRISLYNE MENDES DA VERA CRUZ, ALEXANDRA GABRIELLY DE SOUSA BENTES, ANTONIA PATRICIA OLIVEIRA BARROS, VANESSA SANTOS
LEIOMYOSARCOMA IN THE LATERAL BORDER OF THE TONGUE: A RARE CASE REPORT. CYNTIA HELENA PEREIRA DE CARVALHO, GEORGE BORJA DE FREITAS, HEVIO FREITAS DE LUCENA, KEILA AMORIM BARROSO, BARBARA VANESSA DE BRITO MONTEIRO, LEORIK e FERREIRA DO PEREIRA DA SILVA and, GEORGE JOAO NASCIMENTO Leiomyosarcoma is a rare mesenchymal malignant neoplasm, of which 3% to 10% of cases occur in the head and neck region. The leiomyosarcoma of the tongue is a very rare tumor with only 10 cases described in the literature. This work reports a case of oral leiomyosarcoma arising in the lateral border of the tongue of a 78-year-old man. Clinical examination showed a well-demarcated, firm and painful nodule measuring about 3 cm in diameter. After incisional biopsy, microscopic analysis showed the spindleshaped tumor cells were arranged in an interlacing fascicular pattern and contained oval to elongated blunt-ended (cigar-shaped) nuclei. More than 10 mitoses per high-power field were counted. Immunohistochemical examination displayed that tumor cells were strongly positive to H-caldesmon, actin, and vimentin and negative to S100, establishing the final diagnosis of leiomyosarcoma. The patient was referred for oncologic treatment.
CHONDROID CHORISTOMA IN THE BORDER OF TONGUE: A RARE CASE REPORT. YURI KALININ, NATALIA LACERDA DE OLIVEIRA, CLAUDIA PEREZ TRINDADE FRAGA, MARINA HELENA CURY GALLOTTINI, ANDERSON DA COSTA LINO COSTA, LETICIA DRUMOND DE ABREU e and, OPHIR RIBEIRO JUNIOR GUIMARAES Choristoma is defined as a histologically normal tissue proliferation, which is not normally found in the anatomic site of proliferation. Chondroid choristoma of the oral soft tissue is a rare lesion, presenting cartilage where it is not expected. The patient was a 31-year-old white man presenting an endophytic firm mass on the right lateral border of the tongue also affecting the ventral surface that had appeared 5 years earlier, which was asymptomatic and measured approximately 3 cm in diameter.